Basal sphenoethmoidal encephalocele in association with midline cleft lip and palate: case report* Encefalocele basal esfenoetmoidal associada a fissura labiopalatina mediana: relato de caso
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چکیده
Free and informed consent was obtained from the child’s mother, and the Research Ethics Committee has approved the present study publication. Computed tomography (CT) demonstrated metopic suture diastasis characterizing hypertelorism, and an empty sella turcica occupied by a cystic image. Magthrough the foramen cecum over the cribriform plate of the ethmoid. The second group includes basal encephaloceles with protrusion through the cribriform plate itself or through the sphenoid body. General encephaloceles prevalence is estimated to occur in one of every 35,000 to 40,000 live neonates. The basal presentations, that are even more rarely found, represent only 2% to 10% of such encephaloceles. Considering the rarity of this malformations association, whose treatment leads to high morbidity and mortality, and with few reports in the literature, the authors analyze the clinical and radiological findings of the present case of have cranial dysraphism.
منابع مشابه
Large Sphenoethmoidal Encephalocele Associated with Agenesis of Corpus Callosum and Cleft Palate
Basal encephalocele is a rare craniofacial anomaly. In the present paper we report a 10-year-old boy presented with cleft palate, congenital nystagmus, and hypertelorism. During preoperative evaluation for cleft palate repair, a pulsatile mass was detected in the pharynx. Magnetic resonance imaging showed sphenoethmoidal type of basal encephalocele and agenesis of corpus callosum. Neurosurgical...
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Basal encephaloceles are often associated with other midline anomalies such as hypertelorism, broad nasal root, cleft lip, and cleft palate. Optic disc anomalies such as pallor, dysplasia, optic pit, coLoboma, and megalopapilla have been reported to occur in patients with basal encephalocele We report a case of a child with a sphenoethmoidal encephalocele and morning glory syndrome of the optic...
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AIMS To document the optic disc abnormalities in patients with frontonasal dysplasia in association with basal encephalocele. METHODS Names and hospital numbers of patients with midline clefts were obtained from the ophthalmology and genetics database. Six patients were identified who had the following common findings: midline facial cleft with midline cleft lip and palate; hypertelorism; abs...
متن کاملLarge Sphenoethmoidal Encephalocele Associated with Agenesis of Corpus Callosum and Cleft Palate
Basal encephalocele is a rare craniofacial anomaly. In the present paper we report a 10-year-old boy presented with cleft palate, congenital nystagmus, and hypertelorism. During preoperative evaluation for cleft palate repair, a pulsatile mass was detected in the pharynx. Magnetic resonance imaging showed sphenoethmoidal type of basal encephalocele and agenesis of corpus callosum. Neurosurgical...
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