Basal sphenoethmoidal encephalocele in association with midline cleft lip and palate: case report* Encefalocele basal esfenoetmoidal associada a fissura labiopalatina mediana: relato de caso

نویسندگان

  • Artur Bastos Rocha
  • Rayan Haquim Pinheiro Santos
  • Paulo Germano Cavalcanti Furtado
چکیده

Free and informed consent was obtained from the child’s mother, and the Research Ethics Committee has approved the present study publication. Computed tomography (CT) demonstrated metopic suture diastasis characterizing hypertelorism, and an empty sella turcica occupied by a cystic image. Magthrough the foramen cecum over the cribriform plate of the ethmoid. The second group includes basal encephaloceles with protrusion through the cribriform plate itself or through the sphenoid body. General encephaloceles prevalence is estimated to occur in one of every 35,000 to 40,000 live neonates. The basal presentations, that are even more rarely found, represent only 2% to 10% of such encephaloceles. Considering the rarity of this malformations association, whose treatment leads to high morbidity and mortality, and with few reports in the literature, the authors analyze the clinical and radiological findings of the present case of have cranial dysraphism.

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Large Sphenoethmoidal Encephalocele Associated with Agenesis of Corpus Callosum and Cleft Palate

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تاریخ انتشار 2011